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KMID : 0614720090520010078
Journal of Korean Medical Association
2009 Volume.52 No. 1 p.78 ~ p.90
Spinal Dysraphism and Tethered Cord Syndrome
Kim Dong-Seok

Abstract
Spinal dysraphism is a common birth defect that causes different kinds of secondary impairments, including joint deformities, reduced mobility, and bowel or bladder dysfunction. Various dysraphic spinal abnormalities result in tethered cord syndrome, a progressive form of neurological deterioration that results from spinal cord tethering. The surgery and management of children who have spinal dysraphism require multidisciplinary care and long-term follow-up by multiple specialists in birth defects. This article reviews the clinical presentation, pathophysiology, diagnostic strategies, and therapeutic management of spinal dysraphism in infancy.
KEYWORD
Spinal dysraphism, Neural tube defect, Spina bifida
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